Congenital microtia and atresia of external auditory canal often occur together, which is caused by hypoplasia of the first and second branchial arches or the first branchial groove during embryonic development, and may be accompanied by eustachian tube, tympanum or mastoid malformation caused by hypoplasia of the first pharyngeal sac.

Classification: Type I: The auricle is smaller than normal, and the external auditory canal and tympanic membrane exist, which is acceptable for hearing. Type ⅱ: auricle deformity, atresia of external ear, undeveloped tympanic membrane and malleus stalk, fusion of incus and malleus, with or without stapes. Hearing deafness, which is relatively common. The third type: auricle deformity is serious, external ear atresia, ossicular deformity, combined with non-branchial cleft inner ear deformity. Loss of inner ear function. The second and third types are sometimes accompanied by maxillofacial dysplasia, which is called Terje-Koehler syndrome. Temporal bone CT: external ear atresia, tympanic stenosis, ossicular deformation.

Treatment: the first one can be left untreated, and the second one can be done with external auditory canal plasty and tympanoplasty, so that practical hearing can be obtained after operation. The third type cannot be operated at present because of serious deformity and loss of inner ear function. Those with binaural malformation and good cochlear function should be operated as soon as possible, usually at the age of 2 ~ 5, not too late, so as not to affect language learning. Generally speaking, if one side is deformed and the other side is normal, the operation should be carried out at the age of 8 ~ 9 or later, which is convenient for patients to cooperate. Huier, Zhongshan East Road, Jiaxing, the intersection of Zhongshan Road and Xiuzhou Road, east of CCB.