The opening of myocardial coronary sinus space is a special type of pulmonary atresia, and the ventricular septum is intact, but it is not uncommon, accounting for about 26%, mainly pulmonary atresia with intact ventricular septum. There is no way out for blood to enter the right ventricle from the tricuspid valve. With the increase of right ventricular pressure, tricuspid regurgitation will occur, and some blood will enter the coronary artery through the coronary sinus space and return to the ascending aorta. It's no use taking medicine for this disease. The only way is to open the chest for treatment. What needs special attention is that the surgical plan must not open the occluded pulmonary artery, otherwise, because the coronary artery that perfuses the right heart has adapted to high-pressure perfusion nutrition, as long as the pulmonary artery is opened, the pressure of the right ventricle will drop sharply, which will inevitably lead to blood supply disorder of the right ventricle, and a large area of right ventricular myocardial infarction will occur, leading to death. Single ventricular repair or Fontan operation should be used.

(Dr. Sun Kun solemnly reminds me that because I can't see the patient face to face, I can't fully understand the condition. The above suggestions are for reference only. Please go to the hospital for specific diagnosis and treatment under the guidance of a doctor! )

Shanghai Xinhua Hospital Sun Kun/